Antiphospholipid syndrome (APS) is an autoimmune hypercoagulability syndrome. The clinical feature of the antiphospholipid syndrome is characterized by venous or arterial thromboses, recurrent fetal losses and/or thrombocytopenia with evidence of antiphospholipid antibodies, namely lupus anticoagulant, anticardiolipin antibodies. Although APS is most commonly associated with systemic lupus erythematosus or related autoimmune disease (secondary APS), APS also has been identified in patients with vaso-occlusive disease without any other manifestations of connective tissue disease (primary APS). In primary APS, aortic thrombosis has been rarely reported. We report a case of thrombosis of abdominal aorta in primary APS.

Keywords: Antiphospholipid syndrome, Thrombosis, Abdominal aorta