Case Report
Korean J Hematol 2006; 41(3):
Published online September 30, 2006
https://doi.org/10.5045/kjh.2006.41.3.204
© The Korean Society of Hematology
고용량 부신피질호르몬에 반응을 보인 비혈연골수이식 후의 Evans 증후군
이영호, 김영대, 김영명
한양대학교 서울병원 소아과,
인제백병원 소아과,
동아대병원 소아과
Evans Syndrome following T Cell-repleted Unrelated Bone Marrow Transplantation for Myelodysplastic Syndrome: Successful Response to High-dose Corticosteroid
Evans syndrome after hematopoietic stem cell transplantation rarely occurs and this condition is refractory to treatment, particularly in childhood. We experienced a case of Evans syndrome following unmanipulated unrelated bone marrow transplantation. Evans syndrome developed at early post-transplantation period (day +42) and it responded very well to high-dose corticosteroid. Autoimmune cytopenia should be considered for post-engraftment cytopenias and high-dose corticosteroid therapy might be considered as a treatment of the early onset type of autoimmune cytopenia that can occur after hematopoietic stem cell transplantation.
Keywords Evans syndrome, T cell repleted bone marrow transplantation, High-dose corticosteroid
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Case Report
Korean J Hematol 2006; 41(3): 204-207
Published online September 30, 2006 https://doi.org/10.5045/kjh.2006.41.3.204
Copyright © The Korean Society of Hematology.
고용량 부신피질호르몬에 반응을 보인 비혈연골수이식 후의 Evans 증후군
이영호, 김영대, 김영명
한양대학교 서울병원 소아과,
인제백병원 소아과,
동아대병원 소아과
Evans Syndrome following T Cell-repleted Unrelated Bone Marrow Transplantation for Myelodysplastic Syndrome: Successful Response to High-dose Corticosteroid
Young Ho Lee, Young Dae Kim, Yeong Myung Kim
Department of Pediatrics, Hanyang University Medical Center, Seoul,
Inje University Paik Hospital, Dong, A University Medical Center, Busan, Korea
Abstract
Evans syndrome after hematopoietic stem cell transplantation rarely occurs and this condition is refractory to treatment, particularly in childhood. We experienced a case of Evans syndrome following unmanipulated unrelated bone marrow transplantation. Evans syndrome developed at early post-transplantation period (day +42) and it responded very well to high-dose corticosteroid. Autoimmune cytopenia should be considered for post-engraftment cytopenias and high-dose corticosteroid therapy might be considered as a treatment of the early onset type of autoimmune cytopenia that can occur after hematopoietic stem cell transplantation.
Keywords: Evans syndrome, T cell repleted bone marrow transplantation, High-dose corticosteroid
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