Blood Research

Demographic and baseline laboratory data of the study patients.

Parameter Results
N 22a)
Median age in years (range) 17 (3–72)
Median BAT score (range) 4.5 (3–11)
PT in seconds: mean (±2SD) 13 (±2.83)
aPTT in seconds: mean (±2SD) 30.9 (±6.85)
Fibrinogen level in g/dL: mean (±2SD) 3.17 (±1.43)
Hemoglobin in g/L: median (range) 113 (57–148)
Total leucocyte count ×109/L: median (range) 7.2 (2.7–113.5)
Platelet count ×109/L: median (range) 217 (123–425)
VWF antigen assay: % median (range) 123.05 (68.8–223.6)
VWF GPIbR (RiCoF activity) assay: % median (range) 109.3 (58.7–221.3)

a)Includes 22 non-thrombocytopenic (parallel LTA and FCA data available). Two thrombocytopenic patients (only FCA data available) were discussed separately.

Abbreviations: aPTT, activated partial thromboplastin time; BAT, bleeding assessment tool; PT, prothrombin time; RiCoF, ristocetin cofactor activity assay; VWF, von Willebrand factor.

Blood Res 2021;56:109~118 https://doi.org/10.5045/br.2021.2020232
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