Demographic and baseline laboratory data of the study patients.
Parameter | Results |
---|---|
N | 22a) |
Median age in years (range) | 17 (3–72) |
Median BAT score (range) | 4.5 (3–11) |
PT in seconds: mean (±2SD) | 13 (±2.83) |
aPTT in seconds: mean (±2SD) | 30.9 (±6.85) |
Fibrinogen level in g/dL: mean (±2SD) | 3.17 (±1.43) |
Hemoglobin in g/L: median (range) | 113 (57–148) |
Total leucocyte count ×109/L: median (range) | 7.2 (2.7–113.5) |
Platelet count ×109/L: median (range) | 217 (123–425) |
VWF antigen assay: % median (range) | 123.05 (68.8–223.6) |
VWF GPIbR (RiCoF activity) assay: % median (range) | 109.3 (58.7–221.3) |
a)Includes 22 non-thrombocytopenic (parallel LTA and FCA data available). Two thrombocytopenic patients (only FCA data available) were discussed separately.
Abbreviations: aPTT, activated partial thromboplastin time; BAT, bleeding assessment tool; PT, prothrombin time; RiCoF, ristocetin cofactor activity assay; VWF, von Willebrand factor.