Three prognostic models of AL amyloidosis [12].
Prognostic model | Criteria | Survival |
---|---|---|
Mayo model 2004 [16] | TnT<0.035 μg/L | Stage 1-median 26.4 mo |
NT-pro-BNP<332 ng/L | Stage 2- median 10.5 mo | |
BNP<81 ng/L | Stage 3- median 3.5 mo | |
TnI<0.1 μg/L | ||
Mayo model 2012 [17] | TnT<0.025 ng/mL | Stage 1- median 94.1 mo |
NT-pro-BNP<1,800 pg/mL | Stage 2- median 40.3 mo | |
Serum dFLC<180 mg/dL | Stage 3- median 14 mo | |
BNP<400 ng/L | Stage 4- median 5.8 mo | |
TnI- No data | ||
European model 2015 [18] | TnT<0.035 ng/mL | Stage 1- no death cases |
NT-pro-BNP<332 pg/mL | Stage 2- 3 yr 52% | |
BNP<81 ng/L | Stage 3a- 3 yr 55% | |
TnI<0.1 μg/L | Stage 3b- 3 yr 19% | |
*Mayo 2004 stage 3 has been subclassified based on NT-pro-BNP<8,500 pg/mL | ||
Boston university score 2019 [19] | TnT<0.1 ng/mL | Stage 1- median not reached |
BNP<81 pg/mL | Stage 2- median 9.4 yr | |
Stage 3a- median 4.3 yr | ||
Stage 3b- median 1 yr |