Blood Research

Three prognostic models of AL amyloidosis [12].

Prognostic model Criteria Survival
Mayo model 2004 [16] TnT<0.035 μg/L Stage 1-median 26.4 mo
NT-pro-BNP<332 ng/L Stage 2- median 10.5 mo
BNP<81 ng/L Stage 3- median 3.5 mo
TnI<0.1 μg/L
Mayo model 2012 [17] TnT<0.025 ng/mL Stage 1- median 94.1 mo
NT-pro-BNP<1,800 pg/mL Stage 2- median 40.3 mo
Serum dFLC<180 mg/dL Stage 3- median 14 mo
BNP<400 ng/L Stage 4- median 5.8 mo
TnI- No data
European model 2015 [18] TnT<0.035 ng/mL Stage 1- no death cases
NT-pro-BNP<332 pg/mL Stage 2- 3 yr 52%
BNP<81 ng/L Stage 3a- 3 yr 55%
TnI<0.1 μg/L Stage 3b- 3 yr 19%
*Mayo 2004 stage 3 has been subclassified based on NT-pro-BNP<8,500 pg/mL
Boston university score 2019 [19] TnT<0.1 ng/mL Stage 1- median not reached
BNP<81 pg/mL Stage 2- median 9.4 yr
Stage 3a- median 4.3 yr
Stage 3b- median 1 yr
Blood Res 2020;55:S54~S57 https://doi.org/10.5045/br.2020.S009
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